Single article

Rodionov V., Ivanova I., Budylina M., Egorova I., Kontaurova A.

WILSON'S DISEASES IN THE PRACTICE OF PEDIATRICIAN

Keywords: Wilson's diseases, liver diseases in children, copper, ceruloplasmin, Kayser–Fleischer rings, D-penicillamin

The article is devoted to a rare liver disease – Wilson's Disease. The authors give the definition of the disease; throw light on its etiology, pathogenesis, classification, clinical features, diagnostic criteria, and methods of treatment, providing the evidence of their own observation of Wilson's disease occurrence in a 16-year-old girl, describing the difficulties of diagnosing the case.

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About authors

Rodionov Vladimir Anatolievich
doctor of medical sciences, professor, pediatrics and pediatric surgery department head, Chuvash State University, Russia, Cheboksary (vladimirodionov@yandex.ru)
Budylina Marina Valerievna
candidate of medical sciences, pediatrics and pediatric surgery department associate professor, Chuvash State University, Russia, Cheboksary (M-Budylina2007@yandex.ru)
Egorova Inna Nikolaevna
candidate of medical sciences, pediatrics department associate professor, Chuvash Institute of Advanced Medical Studies, Russia, Cheboksary
Ivanova Irina Evgenievna
doctor of medical sciences, associate professor, pediatrics department head , Institute for Advanced Medical Studies, Russia, Cheboksary
Kontaurova Anna Vladislavovna
pediatrician, Republican Pediatric Clinical Hospital, Russia, Cheboksary

Article link

Rodionov V., Ivanova I., Budylina M., Egorova I., Kontaurova A. WILSON’S DISEASES IN THE PRACTICE OF PEDIATRICIAN [Electronic resource] // Acta medica Eurasica. – 2015. – №3. P. 36-41. – URL: http://acta-medica-eurasica.ru/en/single/2015/3/4/